# STOCKHOLM 1.0 #=GF ID Ndufs5 #=GF AC PF10200.12 #=GF DE NADH:ubiquinone oxidoreductase, NDUFS5-15kDa #=GF AU Coggill P;0000-0001-5731-1588 #=GF GA 21.2 21.2 #=GF NC 21.1 21.1 #=GF TC 21.2 21.2 #=GF SE KOGs (KOG4110) #=GF BM hmmbuild HMM.ann SEED.ann #=GF SM hmmsearch -Z 61295632 -E 1000 --cpu 4 HMM pfamseq #=GF TP Family #=GF WK NADH_dehydrogenase_(ubiquinone) #=GF CL CL0351 #=GF RN [1] #=GF RM 10070614 #=GF RT The human NADH: ubiquinone oxidoreductase NDUFS5 (15 kDa) #=GF RT subunit: cDNA cloning, chromosomal localization, tissue #=GF RT distribution and the absence of mutations in isolated complex #=GF RT I-deficient patients. #=GF RA Loeffen J, Smeets R, Smeitink J, Triepels R, Sengers R, Trijbels #=GF RA F, van den Heuvel L; #=GF RL J Inherit Metab Dis. 1999;22:19-28. #=GF DR INTERPRO; IPR019342; #=GF DR SO; 0100021; polypeptide_conserved_region; #=GF CC This is a family of short, approximately 105 amino acid residue, #=GF CC proteins which form part of NADH:ubiquinone oxidoreductase #=GF CC complex I. Complex I is the first multisubunit inner membrane #=GF CC protein complex of the mitochondrial electron transport chain #=GF CC and it transfers two electrons from NADH to ubiquinone. The #=GF CC protein carries four highly conserved cysteine residues but #=GF CC these do not appear to be in a configuration which would favour #=GF CC metal binding so the exact function of the protein is uncertain #=GF CC [1]. #=GF SQ 677 L8HUI9.1/1-96 MPFFDVQKRL.GVDLDRWMTIQSAEQPHKI.P.SRCHAFEKEWI.EC...A...H...G.I...G.....S..I.....R..A...E....KECKIEF.EDFRECLLRQKTMKR..L...HAI..R....R....Q.R.E...KL......I......KEGK...YTPPP Q02379.2/1-96 MPFFDVQKRL.GVDLDRWMTIQSAEQPHKI.P.SRCHAFEKEWI.EC...A...H...G.I...G.....S..I.....R..A...E....KECKIEF.EDFRECLLRQKTMKR..L...HAI..R....R....Q.R.E...KL......I......KEGK...YTPPP O43920.3/1-96 MPFLDIQKRF.GLNIDRWLTIQSGEQPYKM.A.GRCHAFEKEWI.EC...A...H...G.I...G.....Y..T.....R..A...E....KECKIEY.DDFVECLLRQKTMRR..A...GTI..R....K....Q.R.D...KL......I......KEGK...YTPPP A0A3Q3VJU0.1/1-96 MPFVDLQSRL.GINLDRWLLLQSGEQPNKR.A.ARCHAFEKEWI.EC...A...H...G.I...G.....Q..T.....R..A...K....KECQLEF.EDFYECMHRQKTHQR..L...HAI..R....Q....Q.R.D...KM......L......KEGT...YTPPP A0A667ZAX0.1/1-96 MPFVDLQSRL.GVNLDRWLLLQSGEQPHKR.A.SRCHAFEKEWI.EC...S...H...G.I...G.....Q..T.....R..A...K....QECKVEF.EDFYECMHRQKTHQR..L...HAI..R....Q....Q.R.D...KM......V......KEGT...YTPPP A0A3Q7RNW2.1/1-96 MPFFDVQKRL.GLNLDHWMTIQSAEQPHKI.P.SRCHAFEKEWI.EC...A...H...G.I...G.....A..T.....R..A...E....KECKIEF.DDFVECLLRQKTMKR..L...SDI..R....R....Q.R.D...KL......I......KEGK...YTPPP A0A5F4CCU7.1/1-96 MPFFDVQKRL.GLNLDHWMTIQSAEQPHKI.P.SRCHAFEKEWI.EC...A...H...G.I...G.....A..T.....R..A...E....KECKIEF.DDFVECLLRQKTMKR..L...SDI..R....R....Q.R.D...KL......I......KEGK...YTPPP P0CB87.1/1-96 MPFLDIQKRF.GLNIDRWLTTQSAEQPYKM.A.SRCHAFEKEWI.EC...A...H...G.I...G.....Y..T.....R..A...E....KECKIEY.DDFIECLLRQKTMRR..T...GTI..R....K....Q.R.D...KL......I......KEGK...YTPPP H3CN98.1/1-96 MPFVDLNKRL.GVNLDHWILTQSGPQPHQR.A.ARCHVFEKEWI.EC...S...H...G.I...G.....Q..T.....R..A...K....KECQLEF.EDFYECLHRQKTHQR..L...QAI..R....Q....Q.R.D...KM......V......KEGT...YTPPP A0A2U3X6Z8.1/1-96 MPFFDVQKRL.GLNLDHWMTIQSAEQPHKI.P.GRCHAFEKEWI.EC...A...H...G.I...G.....G..T.....R..A...E....KECKIEF.DDFVECLLRQKTMKR..L...SDI..R....R....Q.R.D...KL......I......KEGK...YTPPP W5QFF9.1/1-96 MPFFDVQKKL.GVDLDHWMTIQSAEQPHRI.P.ARCHAFEKEWI.EC...A...H...G.I...G.....S..I.....R..A...E....KECKIEF.EDFRECLLRQKTMKR..L...NAI..K....R....Q.R.D...KL......I......KEGK...YTPPP Q99LY9.3/1-96 MPFLDIQKKL.GISLDRHFMFLSAEQPYKN.A.ARCHAFEKEWI.EC...A...H...G.I...G.....G..T.....R..A...K....KECKIEF.DDFEECLLRYKTMRR..M...HDI..K....K....Q.R.E...KL......M......KEGK...YTPPP A0A6G1BB28.1/1-96 MPFFDVQKRL.GLNLDHWMTIQSAEQPHKI.P.SRCHAFEKEWI.EC...A...H...G.I...G.....G..T.....R..A...E....KECKIEY.DDFVECLLRHKTMKR..L...NDI..K....R....Q.R.D...KL......I......KEGK...YTPPP Q502P6.1/1-96 MPFIDLQSKL.GINVDKWLLAQSGEQPRKR.A.AFCHAFEKEWI.EC...S...H...A.I...G.....K..T.....R..A...S....KECNIEW.EDFYECMHRFKTMKR..L...KEI..S....T....Q.K.E...KM......I......KEGT...YTPPP A0A4U5VMG5.1/1-95 MPFVDLQTRL.GINLDRWMLLQSGEQPNKR.A.ARCHAFEKEWI.EC...A...H...G.I...G.....Q..T.....R..A...E....KECKLEF.EDFYECMHRQKTHER..L...HAI..R....Q....Q.R.D...KM......I......KEGT...YTPP- A0A2Y9N9T6.1/1-96 MPFFDVQKRL.GLDLDRWMTIQSAEQPHKI.P.GRCHAFEKEWI.EC...A...H...G.I...G.....G..I.....R..A...E....KECKIEY.DDFVECLLRQKTMKR..L...SAI..K....R....Q.R.D...KL......I......KEGK...YTPPP F1SV23.1/1-96 MPFFDVQKRL.GLDLDRWMTIQSAEQPHKI.P.GRCHAFEKEWI.EC...A...H...G.I...G.....G..I.....R..A...E....KECKIEF.DDFVECLLRQKTMKR..L...SAI..K....R....Q.R.D...KL......I......KEGK...YTPPP A0A6I9JZP4.1/1-96 MPFLDVQKRL.GLNVDRWLTVQSAEQPHRL.P.ARCHAFEKEWI.EC...A...H...G.I...G.....G..I.....R..A...E....KECKIEF.DDFSECLLRQKTMKR..M...ATI..K....Q....Q.R.D...KL......I......KEGK...YTPPP A0A5J5N4V6.1/1-96 MPFFDVQKRL.GVDLDHWMTIQGAEQPHRI.P.ARCHAFEKEWI.EC...A...H...G.I...G.....S..T.....R..A...E....KECKIEF.EDFRECLLRQKTMKR..L...NAI..K....R....Q.R.D...KL......I......KEGK...YTPPP A0A4W6FB21.1/1-96 MPFVDVQSRL.GINVDRWLLAQSGPQPNKR.A.ARCHAFEKEWI.EC...A...H...G.I...G.....Q..T.....R..A...K....KECQLEF.EDFYECMHRQKTHER..L...YTI..R....K....Q.R.D...KM......V......KEGT...YTPPP F7AT92.2/6-101 MPFFDVQKRL.GLNLDHWMTIQSAEQPHKI.P.GRCHAFEKEWI.EC...A...H...G.I...G.....G..I.....R..A...E....KECKIEF.DDFVECLLRHKTMKR..L...SAI..R....R....Q.R.D...KL......I......KEGK...YTPPP A0A452R6W0.1/13-108 MPFFDVQKRL.GLNLDHWMTIQTAEQPHKI.P.GRCHAFEKEWI.EC...A...H...G.I...G.....G..T.....R..A...E....KECKIEF.DDFVECLLRQKTMKR..L...SDI..R....R....Q.R.D...KL......I......KEGK...YTPPP A0A4U1EIE4.1/1-96 MPFFDVQKRL.GLDLDRWMTIQSAEQPHKI.P.GRCHAFEKEWI.EC...T...H...G.I...G.....G..I.....R..A...E....KECKIEY.DDFVECLLRQKTMKR..L...SAI..K....R....Q.R.D...KL......I......KEGK...YTPPP A0A6J2LNX0.1/1-96 MPFLDIQKRL.GIDLDRWMTIQSAEQPHRI.P.SRCHAFEKEWI.EC...A...H...G.I...G.....T..I.....R..A...E....KECKLEY.EDFVECMLRQKTMKR..L...STI..M....K....Q.R.D...KL......I......KEGK...YTPPP A0A6A1QB78.1/40-135 MPFFDVQKRL.GLDLDRWMTIQSAEQPHKI.P.GRCHAFEKEWI.EC...A...H...G.I...G.....G..I.....R..A...E....KECKIEF.DDFVECLLRQKTMKR..L...SAI..K....R....Q.R.D...KL......I......KEGK...YTPPP A0A7J8KDA5.1/1-96 MPFFDIQKRL.GVDLDRWMSIQSAEQPHKL.S.SRCHAFEKEWI.EC...A...H...G.I...G.....S..I.....R..A...E....KECKIEY.DDFVECLLRQKTMKR..L...RAI..I....K....Q.R.D...KL......I......KEGK...YTPPP A0A384CCP1.1/1-96 MPFFDVQKRL.GLNLDHWMTIQTAEQPHKI.P.GRCHAFEKEWI.EC...A...H...G.I...G.....G..T.....R..A...E....KECKIEF.DDFVECLLRQKTMKR..L...SDI..R....R....Q.R.D...KL......I......KEGR...YTPPP A0A2F0AVV1.1/50-145 MPFFDVQKRL.GLDLDRWMTIQSAEQPHKI.P.GRCHAFEKEWI.EC...A...H...G.I...G.....G..I.....R..A...E....KECKIEF.DDFVECLLRQKTMKR..L...SAI..K....R....Q.R.D...KL......I......KEGK...YTPPP M3X8I4.2/73-168 MPFFDVQKRL.GLNLDQWMTIQSAEQPHKI.P.GRCHAFEKEWI.EC...A...H...G.I...G.....G..I.....R..A...E....KECKIEY.DDFVECLLRQKTMKR..L...SDI..R....R....Q.R.D...KL......I......KEGK...YTPPP A0A669BUV3.1/1-95 MPFVDLQSRL.GINLDRWLLLQSGEQPNKR.A.ARCHAFEKEWI.EC...S...H...G.I...G.....Q..T.....R..A...K....KECQLEF.EDFYECMHRQKTHER..L...YAI..R....Q....Q.R.D...KL......I......KEGK...YTPP- A0A7J7E3G9.1/59-154 MPFFDVQKRL.GLNLDQWMTIQSAEQPHKI.P.GRCHAFEKEWI.EC...A...H...G.I...G.....G..I.....R..A...E....KECKIEF.DDFVECLLRQKTMKR..L...SAI..K....R....Q.R.D...KL......I......KEGK...YTPPP A0A5N4DD92.1/1-96 MPFFDVQKRL.GLNLDQWMTIQSAEQPNKI.A.GRCHAFEKEWI.EC...A...H...G.I...G.....G..I.....R..A...E....KECKIEY.DDLVECLLRQKTMKR..L...NTI..R....K....Q.R.D...KL......I......KEGK...YTPPP A0A6I9IGW3.1/1-96 MPFFDVQKRL.GLNLDQWMTIQSAEQPNKI.A.GRCHAFEKEWI.EC...A...H...G.I...G.....G..I.....R..A...E....KECKIEY.DDLVECLLRQKTMKR..L...NTI..R....K....Q.R.D...KL......I......KEGK...YTPPP G1LUX2.1/68-163 MPFFDVQKRL.GLNLDHWMTIQTAEQPHKI.P.GRCHAFEKEWI.EC...A...H...G.I...G.....G..T.....R..A...E....KECKIEF.DDFVECLLRQKTMKR..L...SDI..R....R....Q.R.D...KL......I......KEGK...YTPPP A0A5N5KKT0.1/12-106 MPFVDLQSRL.GINLDHWILAQSGEQPYKR.A.TRCHAFEKEWI.EC...G...H...G.I...G.....Q..T.....R..A...K....KECKLEF.EDFYECMHRQKTNKR..L...HEI..R....K....Q.R.D...KL......I......KEGS...YTPP- A0A6P3RDI5.1/1-96 MPFFDIQKRL.GVDLDRWMSIQSAEQPHKL.S.SRCHAFEKEWI.EC...A...H...G.I...G.....F..I.....R..A...E....KECKIEY.DDFVECLLRQKTMKR..L...SAI..M....K....Q.R.D...KL......I......KEGK...YTPPP A0A3Q1AHH5.1/1-95 MPFVDIQSRL.GINVDRWLLLQSGSQPNKR.A.ARCHAFEKEWV.EC...S...H...G.I...G.....Q..T.....R..A...K....KECQLEF.EDFYECMHRQKTHER..L...HAI..R....K....Q.R.D...KL......V......KEGK...YTPP- A0A484CRJ1.1/24-119 MPFVDLQSRL.GINLDSWLLLQSGHQPNKR.A.ARCHAFEKEWI.EC...A...H...D.I...G.....Q..T.....R..A...K....KECQLEF.EDFYECMHRQKTHQR..L...QAI..R....Q....Q.R.D...KM......M......KEGT...YTPPP A0A665WWQ6.1/1-96 MPFVDLQSRL.GINVDRWLLLQSGPQPNKR.A.SRCHAFEKDWI.EC...A...H...G.I...G.....Q..T.....R..A...K....KECKLEF.EDFYECMHRQKTHDR..L...YAI..R....Q....Q.R.D...KL......V......KEGK...YTPPP S9WWE2.1/67-162 MPFFDVQKRL.GLNLDQWMTIQSAEQPNKI.A.GRCHAFEKEWI.EC...A...H...G.I...G.....G..I.....R..A...E....KECKIEY.DDLVECLLRQKTMKR..L...NTI..R....K....Q.R.D...KL......I......KEGK...YTPPP A0A671DZE8.1/59-154 MPFFDIQKRL.GVDLDRWMTIQSAEQPHKL.S.SRCHAFEKEWI.EC...S...H...G.I...G.....V..I.....R..A...E....KECKLEY.DDFVECLLRQKTMKR..L...SAI..M....R....Q.R.D...KL......I......KEGK...YTPPP A0A3Q2DDH7.1/1-95 MPFVDLQSRL.GINVDRWLLLQSGEQPNKR.A.SRCHAFEKEWI.EC...A...H...G.I...G.....Q..T.....R..A...K....KECLMEF.EDFYECMHRQKTHQR..L...YAI..R....Q....Q.R.E...KL......I......KEGK...YTPP- I3MGL4.1/1-96 MPFFDVQKRL.GINLDRHLTIQSADQPYKI.P.SRCHAFEKEWI.EC...A...H...G.I...G.....N..I.....R..A...Q....KECKIEY.EDFVECLLRLKTMKR..V...NTI..K....K....Q.R.D...KL......I......KEGN...YTPPP A0A6G1QXC5.1/1-95 MPFVDLQSKL.GINLDRWMLLQSGEQPNKR.P.ARCHAFEKEWI.EC...A...H...G.I...G.....Q..T.....R..A...K....KECQLEF.EDFYECMHRQKTHQR..L...YTI..R....Q....Q.R.D...KM......I......KEGT...YSPP- A0A3Q3LPN0.2/1-96 MPFVDLQSRL.GINLDQWLLVQSGTQPNNR.A.ARCHAFEKEWI.EC...A...H...G.I...G.....Q..T.....R..A...K....KECQLEF.EDFYECMHRQKTNKR..L...YAI..R....Q....Q.R.D...KM......V......KEGA...YTPPP B5DEL8.1/1-96 MPFLDVQKRL.GISLDRHFIFLSAEQPYKN.A.ARCHAFEKEWI.EC...A...H...G.I...G.....A..T.....R..A...K....KECKIEY.EDFEECFLRFKTIRR..M...HEI..K....K....Q.R.E...KL......M......KEGK...YTPPP A0A3P4RS59.1/58-153 MPFFDVQKRL.GVDLDQWMTIQSAEQPHKI.P.ARCHAFEKEWI.EC...A...H...G.I...G.....A..T.....R..A...A....KECKIEL.DDFAECLLRQKTMKR..L...SEI..R....R....Q.R.N...KL......I......KEGK...YTPPP A0A3Q3EBJ5.1/1-96 MPFVDIQSRL.GINLDRWMLVQSGPQPNNR.P.ARCHAFEKEWI.EC...A...H...G.I...G.....Q..T.....R..A...K....QECKLEF.EDFYECMHRQKTHQR..L...YAI..R....Q....Q.R.A...KM......I......KEGT...YTPPP A0A672Z9V1.1/1-96 MPFVDLQSRL.GINLDRWMLVQSGTQPQKR.A.SRCHAFEKVWI.DC...A...H...G.I...G.....Q..T.....R..A...K....TECQLEF.EDFYECMHRQKTHRR..L...HAI..R....E....Q.R.D...KM......I......KEGT...YTPPP A0A6J2QQU2.1/1-96 MPFLDLQTRL.GINMDKWLLYQSGPQPYKR.A.ARCHAFEKEWI.EC...S...H...S.I...G.....Q..T.....R..A...K....KECQLEF.EDFYECLHKEKTHQR..L...YAI..R....Q....Q.R.D...KM......V......KEGT...YTPPP A0A437CVW4.1/1-95 MPFVDIQSRL.GINVDRWILLQSGEQPNKR.P.ARCHAFEKEWV.EC...S...H...G.I...G.....Q..T.....R..A...K....KECQQEF.EDFYECMHRQKTHRR..L...YAI..R....Q....Q.R.D...KM......I......KEGT...YTPP- A0A2Y9DDB4.1/1-96 MPFFDVQKRL.GLNIDHWMTIQSAEQPYRH.S.ARCHAFEKEWI.EC...A...H...G.I...G.....G..I.....R..A...E....KECKIEF.DDLTECLLRQKTMKR..V...ATI..K....Q....Q.R.A...KL......I......KEGK...YTPPP A0A7J8FA21.1/1-95 MPFFDIQKRL.GIDLDRWMTIQSADQPHKI.P.SRCHAFEKEWI.EC...S...H...G.I...G.....A..I.....R..A...E....KECKIEY.DDFVECLRRQKTMKR..L...SAI..L....R....Q.R.N...KL......I......KEGK...YTPP- A0A3B3H4G2.1/1-96 MPLVDIQSRL.GINVDRWILLQSGEQPNKR.P.ARCHAFEKEWV.EC...S...H...G.I...G.....Q..T.....R..A...K....KECQQEF.EDFYECMHRQKTHQR..L...YAI..R....Q....Q.R.D...KM......I......KEGT...YTPPP A0A2K6F8W8.1/1-96 MPFLDIQKRL.GLDIDRTVTIQSAEQPHKI.P.ARCHAFEKEWI.EC...A...H...G.I...G.....Y..T.....R..A...E....KECKIEY.DDLVECLLRQKTIKR..M...NTI..R....K....Q.R.D...KL......I......KEGK...YTPPP A0A6P3FJN1.1/1-96 MPFFDVQKRL.GISLDRHMTIQSSEQPYRI.A.SRCHAFEKEWL.EC...A...H...G.I...G.....A..T.....R..A...N....KECKIEY.DDLVECLLRQKTMKR..M...SAI..K....K....Q.R.D...KL......I......KEGT...YTPPP A0A5E4A5N2.1/1-96 MPFFDVQKRL.GINLDRHLTIQSADQPYKI.P.SRCHAFEKEWI.EC...A...H...G.I...G.....N..T.....R..A...Q....KECKIEY.EDFVECLLRLKTMKR..V...NTI..K....K....H.R.D...KL......I......KEGN...YTPPP L9JCB9.1/29-123 MPFLDVQKRL.GINIDRWMTIQSGEQPHKL.T.SRCHAFEKEWI.EC...A...H...G.I...G.....S..I.....R..A...E....KECKLEY.DDFIECMVRQKTIKR..M...NAI..R....M....Q.R.E...KL......I......KEGK...YTPP- A0A5E4BN58.1/1-96 MPFFDVQKRL.GINLDRHLTIQSADQPYKI.P.SRCHAFEKEWI.EC...A...H...G.I...G.....N..I.....C..A...Q....KECKIEY.EDFVECLLRLKTMKR..V...NTI..K....K....Q.R.D...KL......I......KEGK...YTPPP A0A5A9NNB9.1/1-96 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